It’s A Rarity! 4 Uncommon Dental Diseases

It’s A Rarity! 4 Uncommon Dental Diseases

The World Health Organization categorizes oral diseases as noncommunicable diseases (NCDs) that affect people throughout their life, causing them pain and discomfort. Oral health diseases were prevalent among half the world’s population in 2016.

And while some oral health concerns are common, like periodontal diseases, cavities, bruxism, and others, there are others that are not diagnosed until it’s too late.

Visits to the dentist usually include cleaning, fillings and, if needed, dental implants and tooth extractions. Rarely are we diagnosed with the following diseases—but that does not mean that they don’t occur among an unfortunate few:


Hyperdontia is a rare condition where a patient develops more than 32 permanent teeth. Those who develop this condition usually have one extra tooth behind the upper, front teeth. If not extracted, this tooth will cause pain and impact the adjacent permanent teeth.

According to research, around 80 to 93% of hyperdontia (supernumerary teeth) cases cause complications and affect the overall health of the patient. Early diagnosis and clinical interventions can reduce the impact on adjacent teeth.

Papillon Lefevre Syndrome (PLS)

Papillon Lefevre Syndrome is a rare genetic disorder that becomes apparent between the ages of one to five. Children and teenagers with PLS develop dry scaly patches on the skin of their palms and soles.

PLS also leads to inflammation and degeneration of the enamel, dentine, and roots, which are responsible for providing protection and support to your teeth.

When PLS fully sets in, the primary teeth become loose and completely fall out by the age of five. If left untreated, the primary teeth may also fall out by the age of seventeen. People with PLS may opt to remove all their remaining teeth and get fitted with dentures.

Otodental Syndrome

Otodental Syndrome is a rare genetic disorder that impacts a patient’s hearing as well as their teeth. In this condition, canines and molars become enlarged to the point that they impact the entire facial structure. This may also result in overcrowding in the jaw, displacing adjacent teeth from their space.

The treatment for Otodental Syndrome is complex and often involves tooth extractions and repairs by an experienced orthodontist.

Gingival Fibromatosis

Just like PLS, Gingival Fibromatosis is also a hereditary oral disease that causes the overgrowth of gum tissues. The gums appear extremely puffy and swollen, which may also affect speech. In some cases, these swollen gums can cover the entire teeth and cause extreme pain.

Here, at Bethesda Health, our dentists can take care and provide treatments to treat you for any dental illness. Our services include tooth extraction, dental implants and veneers services in Bethesda, Maryland. Get in touch with us today!


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